Sickle Cell Disease

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Current Evidence and Rationale to Guide Perioperative Management, Including Transfusion Decisions, in Patients With Sickle Cell Disease

The anaesthetic management of children with sickle cell disease

A Comparison of Conservative and Aggressive Transfusion Regimens in the Perioperative Management of Sickle Cell Disease

Sickle Cell Disease and Anesthesia

Anaesthetic management of children with sickle cell disease

Special issue: Pediatric pain and sickle cell disease

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APSF: Preoperative Transfusion and Sickle Cell Disease in the Pediatric Patient

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4. Azbell RCG, Lanzkron SM, Desai PC. Current Evidence and Rationale to Guide Perioperative Management, Including Transfusion Decisions, in Patients With Sickle Cell Disease. Anesthesia and analgesia 2023;136(6):1107-1114. (In eng). DOI: 10.1213/ane.0000000000006463.

5. Baijal RG, Dalal PG, Kanjia M. Preoperative Transfusion and Sickle Cell Disease in the Pediatric Patient. Anesthesia Patient Safety Foundation. 06/2024 (https://www.apsf.org/article/preoperative-transfusion-and-sickle-cell-disease-in-the-pediatric-patient/?utm_source=APSF+Newsletter+Email+-+External&utm_medium=email&utm_campaign=EMAIL_CAMPAIGN_2024_06_01).

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7. Waldron P, Pegelow C, Neumayr L, et al. Tonsillectomy, adenoidectomy, and myringotomy in sickle cell disease: perioperative morbidity. Preoperative Transfusion in Sickle Cell Disease Study Group. JPediatrHematolOncol 1999;21(2):129-135.

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9. Salvi PS, Solomon DG, Cowles RA. Preoperative Transfusion and Surgical Outcomes for Children with Sickle Cell Disease. J Am Coll Surg 2022;235(3):530-538. (In eng). DOI: 10.1097/xcs.0000000000000267.

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Howard J, Hart N, Roberts-Harewood M, et al. Guideline on the management of acute chest syndrome in sickle cell disease. Br J Haematol. 2015 May; 169(4): 492-505. PMID: 25824256

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Sohn E. Ease the Pain: The excruciating pain of sickle cell disease is difficult to prevent or treat. Researchers are working on new ways to provide relief. Sci Am 2024; 331(3): 94.

Reardon S. New Treatments for Sickle Cell Disease: After years of little progress, new therapies to treat or even cure the disease are reaching patients. Sci Am 2024; 331(3): 85.

Smith WR, Penberthy LT, Bovbjerg VE, et al. Daily assessment of pain in adults with sickle cell disease. Annals of internal medicine 2008; 148(2): 94-101.

Smith WR, Scherer M. Sickle-Cell Pain: Advances in Epidemiology and Etiology. Hematology 2010; 2010(1): 409-15.

Dampier C, Ely E, Brodecki D, O'Neal P. Home management of pain in sickle cell disease: a daily diary study in children and adolescents. J Pediatr Hematol Oncol 2002; 24(8): 643-7.

Brandow AM, Brousseau DC, Panepinto JA. Postdischarge pain, functional limitations and impact on caregivers of children with sickle cell disease treated for painful events. Br J Haematol 2009; 144(5): 782-8.

Ballas SK, Lusardi M. Hospital readmission for adult acute sickle cell painful episodes: frequency, etiology, and prognostic significance. Am J Hematol 2005; 79(1): 17-25.

Dampier CD, Telen MJ, Wun T, et al. A randomized clinical trial of the efficacy and safety of rivipansel for sickle cell vaso-occlusive crisis. Blood 2023; 141(2): 168-79.

Karimi M, Bahadoram M, Mafakher L, Rastegar M. Impact of Imatinib on reducing the painful crisis in patients with sickle cell disease. Hematol Transfus Cell Ther 2024; 46(4): 387-92.

"First Patient Begins Newly Approved Sickle Cell Gene Therapy." The New York Times, May 6, 2024.